Coronary abnormalities in hyper-IgE recurrent infection syndrome: depiction at coronary MDCT angiography
AM Gharib, RI Pettigrew, A Elagha… - American Journal of …, 2009 - Am Roentgen Ray Soc
American Journal of Roentgenology, 2009•Am Roentgen Ray Soc
OBJECTIVE. Hyper-IgE recurrent infection syndrome (HIES or Job's syndrome) is a rare
disorder affecting the immune system and connective tissues. The purpose of this study is to
describe the coronary abnormalities in genetically confirmed HIES patients as depicted by
coronary MDCT angiography (MDCTA). CONCLUSION. Coronary MDCTA has provided an
opportunity for noninvasive evaluation of the coronary arteries in patients with HIES. These
coronary abnormalities vary from tortuosity to ectatic dilation and focal aneurysms of the …
disorder affecting the immune system and connective tissues. The purpose of this study is to
describe the coronary abnormalities in genetically confirmed HIES patients as depicted by
coronary MDCT angiography (MDCTA). CONCLUSION. Coronary MDCTA has provided an
opportunity for noninvasive evaluation of the coronary arteries in patients with HIES. These
coronary abnormalities vary from tortuosity to ectatic dilation and focal aneurysms of the …
OBJECTIVE. Hyper-IgE recurrent infection syndrome (HIES or Job's syndrome) is a rare disorder affecting the immune system and connective tissues. The purpose of this study is to describe the coronary abnormalities in genetically confirmed HIES patients as depicted by coronary MDCT angiography (MDCTA).
CONCLUSION. Coronary MDCTA has provided an opportunity for noninvasive evaluation of the coronary arteries in patients with HIES. These coronary abnormalities vary from tortuosity to ectatic dilation and focal aneurysms of the coronary arteries. Such an evaluation has potential value in identifying new aspects of this disease and thereby providing better understanding of the pathophysiology of the disorder.
Am Roentgen Ray Soc
